GynecologyGynecologyГинекология2079-56962079-5831Consilium Medicum3012010.26442/2079-5696_2018.5.56-58ArticlesСтатьиReview ArticlePossibilities of preservation and realization of reproductive function in girls with Turner syndrome (analytical review)Возможности сохранения и реализации репродуктивной функции у девочек с синдромом Тернера (аналитический обзор)KumykovaZ KhКумыковаЗаира Хасановна

канд. мед. наук, ст. науч. сотр. 2-го гинекологического отд-ния (гинекологии детского и юношеского возраста)

zai-kumykova@yandex.ruBatyrovaZ KБатыроваЗалина Кимовна

канд. мед. наук, науч. сотр. 2-го гинекологического отд-ния (гинекологии детского и юношеского возраста)

linadoctor@mail.ruV.I.Kulakov National Medical Research Center for Obstetrics, Gynecology and Perinatology of the Ministry of Health of the Russian FederationФГБУ «НМИЦ АГП им. акад. В.И.Кулакова»15102018205VOL 20, NO5 (2018)ТОМ 20, №5 (2018)565809042020Copyright ©; 2018, Consilium MedicumCopyright ©; 2018, ООО "Консилиум Медикум"2018Consilium MedicumООО "Консилиум Медикум"https://creativecommons.org/licenses/by-nc-sa/4.0https://gynecology.orscience.ru/2079-5831/article/view/30120

Turner syndrome (TS) is the most common chromosomal abnormality in females. TS is associated with partial or complete loss of the second X-chromosome in phenotypic females and is associated with increased morbidity and mortality. There are many controversial issues of monitoring, management and counseling of patients with TS. This review emphasizes the need for a multidisciplinary approach to the study of this pathology to enable the realization of reproductive function in patients with TS.

Синдром Тернера (СТ) является наиболее распространенной хромосомной аномалией у женщин. СТ ассоциирован с частичной или полной потерей второй Х-хромосомы у фенотипических женщин и связан с увеличением заболеваемости и смертности. Существует много дискуссионных вопросов наблюдения, ведения и консультирования пациенток с СТ. Этот обзор подчеркивает необходимость мультидисциплинарного подхода к изучению данной патологии для обеспечения возможностей реализации репродуктивной функции пациенток с СТ.

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